CEREBRAL CAVERNOUS ANGIOMAS - AN ATYPICAL CASE IN INFANCY

Cerebral cavernous angiomas (CCA) are rare, reportedly accounting for only 1% of all intracranial vascular lesions and 15% of all cerebral v ascular malformations. Forms are sporadic or familial, and the mode of inheritance is probably autosomal dominant. We report an unusual case of an infant born ar 37 weeks of gestational age following a normal p regnancy. Her birthweight was 1560 g. The family history was negative. At 10 months of age, the child presented with the sudden onset of mus cular hypotonia, motility and strength deficits, and absence of osteot endinous reflexes in the right arm. The psychomotor development of the child was normal. MRI revealed the presence of a cavernous angioma in the paramedian pontine region. The child's monoparesis quickly disapp eared. This case is interesting because of the age at onset and the wa y in which the clinical manifestations developed.