G. Stafanger et al., CONVERSION OF THE MODIFIED FONTAN OPERATION TO TOTAL CAVOPULMONARY CONNECTION - A TREATMENT FOR PROTEIN-LOSING ENTEROPATHY, Cardiology in the young, 7(3), 1997, pp. 344-346
We describe a patient with tricuspid atresia who, after a Fontan opera
tion three years earlier, presented with severe protein-losing enterop
athy. After conversion to a cavopulmonary connection, the symptoms reg
ressed and substitution with albumin and immunoglobulin was no longer
required.