MR OF THE BRAIN IN SJOGREN-LARSSON-SYNDROME

Cerebral MR was performed in three patients with Sjogren-Larsson syndr ome, In each case, a 1,5-T system was used, and the patient was under general anesthesia, The MR findings included confluent hyperintense wh ite matter lesions in the periventricular and deep white matter of the centrum semi-ovale, with sparing of the subcortical U fibers, The top ography of the white matter abnormalities correlated well with the cli nical signs and symptoms.