MULTIPLE VASCULAR LEIOMYOMAS INVOLVING BILATERAL ADRENAL-GLANDS, SPLEEN, AND EPICARDIUM, ASSOCIATED WITH BILATERAL TESTICULAR MICROLITHIASIS AND EMPTY SELLA TURCICA

Leiomyomas can arise from any tissue having smooth muscle as one of it s constituents, especially gastrointestinal and genitourinary systems, less frequently in the skin, and rarely in deep soft tissue. An unusu al case of multiple vascular leiomyomas involving bilateral adrenal gl ands, spleen, and epicardium, associated with bilateral testicular mic rolithiasis, and empty sella turcica is reported in a 15-year-old boy. The adrenal masses were incidentally discovered by ultrasonography. T hese three findings, taken individually are rare, and the constellatio n of the th ree, to the best of our knowledge, is the first recorded e xample. Furthermore, bilateral involvement of the adrenal glands with leiomyomas is, by itself, very uncommon. The tumors considered benign were surgically removed. Orchiectomy wasn't performed. The boy is well after 1.5-year follow-up under cortisone, 9 alpha-fludrocortisone, an d testosterone therapy. Copyright (C) 1997 by W.B. Saunders Company.