SIMPLE CHORISTOMA OF THE ANTERIOR SEGMENT CONTAINING BRAIN-TISSUE

We report an unusual case of a simple choristoma of the anterior segme nt that contained only brain tissue. The clinical characteristics and findings of pathological examination of this unusual ocular malformati on were reviewed. A newborn girl was seen with a fleshy, highly vascul ar cystic mass arising from the inferior limbus and extending across t he cornea. On a computed tomographic scan, gross disruption of the ant erior segment was present, with subluxation of the lens into the cyst. Excision of the abnormal tissue was followed by evisceration; polygla ctin (Vicryl) ball implantation; patch graft of the globe; and, later, prosthetic fitting. Pathologic findings showed a choristomatous malfo rmation, containing only mature brain tissue. To our knowledge, a chor istoma in which the sole constituent is brain tissue has not previousl y been reported.