RECURRENT INTRACRANIAL EPITHELIOID HEMANGIOENDOTHELIOMA ASSOCIATED WITH MULTICENTRIC DISEASE OF LIVER AND HEART - CASE-REPORT

EPITHELIOID HEMANGIOENDOTHELIOMA IS an unusual vascular neoplasm with prominent cytoplasmic vacuolization representing primitive lumen forma tion. A case is presented of this unique vascular neoplasm in a woman with a seizure disorder who had cardiac, hepatic, and recurrent nervou s system lesions. To our knowledge, this is the third known case of in tracranial epithelioid hemangioendothelioma. Emphasis is placed on the indolent course of this rare neoplasm, with a recommendation for aggr essive surgical treatment and diligent follow-up.