A 43-year-old man presented with a tumour of the medial part of the ri
ght eyebrow. A biopsy was performed and histological examination revea
led a malignant transformation of a 'calcifying epithelioma of Malherb
e'. A secondary wide excision was performed. Clinical and pathological
findings of this extremely rare tumour are reviewed. Factors influenc
ing the prognosis are proposed, based on a compilation of the literatu
re.