We report the case of a 14-year-old boy with granulomatous pneumonia c
aused by Francisella tularensis. In addition, an autosomal recessive f
orm of chronic granulomatous disease was diagnosed. Both F. tularensis
and chronic granulomatous disease are associated with pulmonary granu
lomas. To our knowledge, this is the first report of F. tularensis inf
ection in a patient with chronic granulomatous disease. The relationsh
ip between these two processes is discussed.