A case of hydrometrocolpos with vaginal opening to the bladder is pres
ented. A newborn female presented abdominal distention and postaxial p
olydactyly at birth. Clinical investigation revealed hydrometrocolpos,
precocious puberty, urogenital sinus and other multiple malformations
. The vagina was open to the bladder with a small orifice, Vaginal pul
l-through surgery and closure of the communication was performed. Over
a hundred cases of hydrometrocolpos have been reported previously. Ho
wever, we could not find a case of hydrometrocolpos with vaginal openi
ng to the bladder among them.