Djl. Macgowan et al., ISOLATED MYOCLONIC ALIEN HAND AS THE SOLE PRESENTATION OF PATHOLOGICALLY ESTABLISHED CREUTZFELDT-JAKOB-DISEASE - A REPORT OF 2 PATIENTS, Journal of Neurology, Neurosurgery and Psychiatry, 63(3), 1997, pp. 404-407
Creutzfeldt-Jakob disease may have many atypical presentations before
the development of classic progressive dementia and startle myoclonus.
In two patients with pathologically established disease association w
ith a progressive alien hand syndrome was the sole initial manifestati
on of the disease.