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Results: 1-15 |
Results: 15
Substrate reduction therapy for glycosphingolipid storage disorders
Authors: Lachmann, RH Platt, FM
Citation: Rh. Lachmann et Fm. Platt, Substrate reduction therapy for glycosphingolipid storage disorders, EXPERT OP I, 10(3), 2001, pp. 455-466
Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy
Authors: Platt, FM Jeyakumar, M Andersson, U Priestman, DA Dwek, RA Butters, TD Cox, TM Lachmann, RH Hollak, C Aerts, JMFG Van Weely, S Hrebicek, M Moyses, C Gow, I Elstein, D Zimran, A
Citation: Fm. Platt et al., Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy, J INH MET D, 24(2), 2001, pp. 275-290
N-butyldeoxynojirimycin reduces growth and ganglioside content of experimental mouse brain tumours
Authors: Ranes, MK El-Abbadi, M Manfredi, MG Mukherjee, P Platt, FM Seyfried, TN
Citation: Mk. Ranes et al., N-butyldeoxynojirimycin reduces growth and ganglioside content of experimental mouse brain tumours, BR J CANC, 84(8), 2001, pp. 1107-1114
Enhanced survival in Sandhoff disease mice receiving a combination of substrate deprivation therapy and bone marrow transplantation
Authors: Jeyakumar, M Norflus, F Tifft, CJ Cortina-Borja, M Butters, TD Proia, RL Perry, VH Dwek, RA Platt, FM
Citation: M. Jeyakumar et al., Enhanced survival in Sandhoff disease mice receiving a combination of substrate deprivation therapy and bone marrow transplantation, BLOOD, 97(1), 2001, pp. 327-329
High-performance liquid chromatography analysis of ganglioside carbohydrates at the picomole level after ceramide glycanase digestion and fluorescentlabeling with 2-aminobenzamide
Authors: Wing, DR Garner, B Hunnam, V Reinkensmeier, G Andersson, U Harvey, DJ Dwek, RA Platt, FM Butters, TD
Citation: Dr. Wing et al., High-performance liquid chromatography analysis of ganglioside carbohydrates at the picomole level after ceramide glycanase digestion and fluorescentlabeling with 2-aminobenzamide, ANALYT BIOC, 298(2), 2001, pp. 207-217
Imino sugar therapy for type 1 Gaucher disease
Authors: Priestman, DA Platt, FM Dwek, RA Butters, TD
Citation: Da. Priestman et al., Imino sugar therapy for type 1 Gaucher disease, GLYCOBIOLOG, 10(11), 2000, pp. IV-VI
Molecular requirements of imino sugars for the selective control of N-linked glycosylation and glycosphingolipid biosynthesis
Authors: Butters, TD van den Broek, LAGM Fleet, GWJ Krulle, TM Wormald, MR Dwek, RA Platt, FM
Citation: Td. Butters et al., Molecular requirements of imino sugars for the selective control of N-linked glycosylation and glycosphingolipid biosynthesis, TETRAHEDR-A, 11(1), 2000, pp. 113-124
Mutations at critical N-glycosylation sites reduce tyrosinase activity by altering folding and quality control
Authors: Branza-Nichita, N Negroiu, G Petrescu, AJ Garman, EF Platt, FM Wormald, MR Dwek, RA Petrescu, SM
Citation: N. Branza-nichita et al., Mutations at critical N-glycosylation sites reduce tyrosinase activity by altering folding and quality control, J BIOL CHEM, 275(11), 2000, pp. 8169-8175
Inhibition of glycosphingolipid biosynthesis: Application to lysosomal storage disorders
Authors: Butters, TD Dwek, RA Platt, FM
Citation: Td. Butters et al., Inhibition of glycosphingolipid biosynthesis: Application to lysosomal storage disorders, CHEM REV, 100(12), 2000, pp. 4683
N-butyldeoxygalactonojirimycin: A more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo
Authors: Andersson, U Butters, TD Dwek, RA Platt, FM
Citation: U. Andersson et al., N-butyldeoxygalactonojirimycin: A more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo, BIOCH PHARM, 59(7), 2000, pp. 821-829
High-performance cation-exchange chromatography and pulsed amperometric detection for the separation, detection, and quantitation of N-alkylated imino sugars in biological samples
Authors: Mellor, HR Adam, A Platt, FM Dwek, RA Butters, TD
Citation: Hr. Mellor et al., High-performance cation-exchange chromatography and pulsed amperometric detection for the separation, detection, and quantitation of N-alkylated imino sugars in biological samples, ANALYT BIOC, 284(1), 2000, pp. 136-142
Chemical plug for zone isolation in horizontal wells
Authors: Mamora, DD Saavedra, NF Burnett, DB Platt, FM
Citation: Dd. Mamora et al., Chemical plug for zone isolation in horizontal wells, J ENERG RES, 121(1), 1999, pp. 40-44
Imino sugars inhibit the formation and secretion of bovine viral diarrhea virus, a pestivirus model of hepatitis C virus: Implications for the development of broad spectrum anti-hepatitis virus agents
Authors: Zitzmann, N Mehta, AS Carrouee, S Butters, TD Platt, FM McCauley, J Blumberg, BS Dwek, RA Block, TM
Citation: N. Zitzmann et al., Imino sugars inhibit the formation and secretion of bovine viral diarrhea virus, a pestivirus model of hepatitis C virus: Implications for the development of broad spectrum anti-hepatitis virus agents, P NAS US, 96(21), 1999, pp. 11878-11882
Delayed symptom onset and increased life expectancy in Sandhoff disease mice treated with N-butyldeoxynojirimycin
Authors: Jeyakumar, M Butters, TD Cortina-Borja, M Hunnam, V Proia, RL Perry, VH Dwek, RA Platt, FM
Citation: M. Jeyakumar et al., Delayed symptom onset and increased life expectancy in Sandhoff disease mice treated with N-butyldeoxynojirimycin, P NAS US, 96(11), 1999, pp. 6388-6393
Tyrosinase folding and copper loading in vivo: A crucial role for calnexinand alpha-glucosidase II
Authors: Branza-Nichita, N Petrescu, AJ Dwek, RA Wormald, MR Platt, FM Petrescu, SM
Citation: N. Branza-nichita et al., Tyrosinase folding and copper loading in vivo: A crucial role for calnexinand alpha-glucosidase II, BIOC BIOP R, 261(3), 1999, pp. 720-725
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