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Results: 1-23 |
Results: 23

Authors: COSTEFF H APTER N ELPELEG ON PRIALNIC M BOHLES HJ
Citation: H. Costeff et al., INEFFECTIVENESS OF ORAL COENZYME-Q10 SUPPLEMENTATION IN 3-METHYLGLUTACONIC ACIDURIA, TYPE-3, Brain & development, 20(1), 1998, pp. 33-35

Authors: HENNERMANN JB HERWIG J MARZ W ASSKALI F BOHLES HJ
Citation: Jb. Hennermann et al., LIPID AND LIPOPROTEIN PROFILES IN CHILDREN WITH FAMILIAL HYPERCHOLESTEROLEMIA - EFFECTS OF THERAPY, European journal of pediatrics, 157(11), 1998, pp. 912-918

Authors: KNERR IM HERWIG J SEWELL AC ZINN C REITTER B BOHLES HJ
Citation: Im. Knerr et al., DEXTROMETHORPHAN THERAPY IN NONKETOTIC HY PERGLYCINEMIA - 4 CASE-HISTORIES, Monatsschrift fur Kinderheilkunde, 146(2), 1998, pp. 100-104

Authors: WEIMANN E BOHLES HJ
Citation: E. Weimann et Hj. Bohles, ESTROGEN-TREATMENT OF TALL STATURE - REPLY, Archives of Disease in Childhood, 79(2), 1998, pp. 199-199

Authors: WEIMANN E BERGMANN S BOHLES HJ
Citation: E. Weimann et al., ESTROGEN-TREATMENT OF CONSTITUTIONAL TALL STATURE - A RISK-BENEFIT RATIO, Archives of Disease in Childhood, 78(2), 1998, pp. 148-151

Authors: ARNDT S SEWELL AC EHRENFORTH S WENKE A SCHARRER I BOHLES HJ GOETHE JW
Citation: S. Arndt et al., HYPERHOMOCYSTEINEMIA IN JUVENILE VENOUS THROMBOSIS - METHIONINE INTOLERANCE AND VITAMIN SUPPLEMENTATION, Thrombosis and haemostasis, 1997, pp. 2172-2172

Authors: DRIEVER PH GOHLICHRATMANN G KONIG R HELLER K SCHMIDT H BAUM RP BOHLES HJ
Citation: Ph. Driever et al., CONGENITAL MICROGASTRIA, GROWTH-HORMONE DEFICIENCY AND DIABETES-INSIPIDUS, European journal of pediatrics, 156(1), 1997, pp. 37-40

Authors: WEIMAN E MOLENKAMP G BOHLES HJ
Citation: E. Weiman et al., DIABETES-INSIPIDUS DUE TO HYPOPHYSITIS, Hormone research, 47(2), 1997, pp. 81-84

Authors: BOEHM G MULLER H KOHN G MORO G MINOLI I BOHLES HJ
Citation: G. Boehm et al., DOCOSAHEXAENOIC AND ARACHIDONIC-ACID ABSORPTION IN PRETERM INFANTS FED LCP-FREE OR LCP-SUPPLEMENTED FORMULA IN COMPARISON TO INFANTS FED FORTIFIED BREAST-MILK, Annals of nutrition & metabolism, 41(4), 1997, pp. 235-241

Authors: SEWELL AC HERWIG J BOHLES HJ SPERL W
Citation: Ac. Sewell et al., MITOCHONDRIAL RESPIRATORY-CHAIN SUCCINATE-CYTOCHROME-C OXIDOREDUCTASEDEFICIENCY AND HEPATIC CIRRHOSIS, Journal of inherited metabolic disease, 20(6), 1997, pp. 837-838

Authors: SEWELL AC SPERL W HERWIG J BOHLES HJ
Citation: Ac. Sewell et al., CIRRHOSIS IN A CHILD WITH DEFICIENCY OF MITOCHONDRIAL RESPIRATORY-CHAIN SUCCINATE CYTOCHROME-C OXIDOREDUCTASE, The Journal of pediatrics, 131(1), 1997, pp. 166-168

Authors: BOEHM G BORTE M BOHLES HJ MULLER H KOHN G MORO G
Citation: G. Boehm et al., DOCOSAHEXAENOIC AND ARACHIDONIC-ACID CONTENT OF SERUM AND RED-BLOOD-CELL MEMBRANE PHOSPHOLIPIDS OF PRETERM INFANTS FED BREAST-MILK, STANDARD FORMULA OR FORMULA SUPPLEMENTED WITH N-3 AND N-6 LONG-CHAIN POLYUNSATURATED FATTY-ACIDS, European journal of pediatrics, 155(5), 1996, pp. 410-416

Authors: BECKER S FUNK M POTZSCH B JOSEPHSTEINER J BOHLES HJ KREUZ W
Citation: S. Becker et al., THROMBOPHILIA ASSOCIATED WITH CDG-SYNDROME TYPE-I, Thrombosis and haemostasis, 73(6), 1995, pp. 1401-1401

Authors: SEWELL AC BOHLES HJ HERWIG J DEMIRKOL M
Citation: Ac. Sewell et al., NEUROLOGICAL DETERIORATION IN PATIENTS WITH UREA CYCLE DISORDERS UNDER VALPROATE THERAPY - A CAUSE FOR CONCERN, European journal of pediatrics, 154(7), 1995, pp. 593-594

Authors: SEWELL AC BOHLES HJ
Citation: Ac. Sewell et Hj. Bohles, ACYLCARNITINES IN INTERMEDIARY METABOLISM, European journal of pediatrics, 154(11), 1995, pp. 871-877

Authors: KOCH A DORR HG GERLING S BEHRENS R BOHLES HJ
Citation: A. Koch et al., EFFECT OF GROWTH-HORMONE ON IGF-I LEVELS IN A PATIENT WITH GROWTH-HORMONE DEFICIENCY AND WILSON DISEASE, Hormone research, 44(1), 1995, pp. 40-44

Authors: HOFFMANN GF BOHLES HJ BURLINA A DURAN M HERWIG J LEHNERT W LEONARD JV MUNTAU A PLECKOSTARTING FK SUPERTIFURGA A TREFZ FK CHRISTENSEN E
Citation: Gf. Hoffmann et al., EARLY SIGNS AND COURSE OF DISEASE OF GLUTARYL-COA DEHYDROGENASE-DEFICIENCY, Journal of inherited metabolic disease, 18(2), 1995, pp. 173-176

Authors: HESSE V BOHLES HJ SEWELL AC FORSTER H JANISCH W MIDDLETON D HABERLAND H
Citation: V. Hesse et al., 11-BETA-KETOTHIOLASE DEFICIENCY WITH OBSTRUCTIVE CARDIOMYOPATHY AND SPECIFIC MORPHOLOGICAL BRAIN, Pediatric research, 35(2), 1994, pp. 267-267

Authors: WEISE M JAMES D HARTMANN KH REINHARDT D LEITNER C BOHLES HJ ATTANASIO A
Citation: M. Weise et al., DOSE-DEPENDENT EFFECT OF GROWTH-HORMONE THERAPY ON GLUCOSE-METABOLISMIN SUBJECTS WITH TURNER SYNDROME, Hormone research, 39, 1993, pp. 25-29

Authors: WEISE M JAMES D LEITNER CH HARTMANN KKP BOHLES HJ ATTANASIO A BIERMANNFRANKE H BEYER P BOEHLES HJ BRAEMSWIG J BRENDEL L BUTENANDT O DOERR HG ENGLERT V EPPING W HAHN C HARTMANN KKP HAUFFA BP HECKER W HEINRICH U HENRICHS I HOMOKI J IRLE U KNOEBL D KOLLMANN F KRUSE K KUNZE D LEITNER C MENKEN U MUEHLENBERG R VONMUEHLENDAHL KE RAGER K RANKE MB REINHARDT D STAHNKE N STOLECKE H TIETZE HU WENDEL U WILLIG RP
Citation: M. Weise et al., GLUCOSE-METABOLISM IN ULLRICH-TURNER SYNDROME - LONG-TERM EFFECTS OF THERAPY WITH HUMAN GROWTH-HORMONE, Hormone research, 39(1-2), 1993, pp. 36-41

Authors: GHEITH S SCHARF J BOHLES HJ HOHMANN B RUDER H
Citation: S. Gheith et al., CONTINUOUS VENOVENOUS HEMOFILTRATION (CVVH) AND METHYLMALONIC ACIDEMIA, Nieren- und Hochdruckkrankheiten, 22(4), 1993, pp. 164-166

Authors: MARZ W BAUMSTARK MW SCHARNAGL H RUZICKA V BUXBAUM S HERWIG J POHL T RUSS A SCHAAF L BERG A BOHLES HJ USADEL KH GROSS W
Citation: W. Marz et al., ACCUMULATION OF SMALL DENSE LOW-DENSITY LIPOPROTEINS (LDL) IN A HOMOZYGOUS PATIENT WITH FAMILIAL DEFECTIVE APOLIPOPROTEIN B-100 RESULTS FROM HETEROGENOUS INTERACTION OF LDL SUBFRACTIONS WITH THE LDL RECEPTOR, The Journal of clinical investigation, 92(6), 1993, pp. 2922-2933

Authors: BADENHOOP K NICOLAY A HERWIG J BOHLES HJ USADEL KH
Citation: K. Badenhoop et al., POLYMORPHISMS OF TAP (TRANSPORTERS ASSOCIATED WITH ANTIGEN-PROCESSING) GENES IN TYPE-1 DIABETES-MELLITUS, Diabetologia, 36, 1993, pp. 10000017-10000017
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